Lung Transplantation for Pleuroparenchymal Fibroelastosis

Civil Hospices of Lyon

Status: Unknown

Conditions: Fibroelastosis

Treatments: Procedure: Lung transplantation (single, lobar or bilateral lung transplantation)

Study type: Observational

Funder types: Other

Identifiers

NCT05044390

420

Details and patient eligibility

About

This retrospective observational study will evaluate the outcomes of lung transplantation for a rare cause of interstitial lung disease called pleuroparenchymal fibroelastosis. Data will be collected from all transplantation center in France.

Enrollment: 30 estimated patients

Sex: All

Volunteers: No Healthy Volunteers

Inclusion criteria

• Lung transplantation (any type) for pleuroparenchymal fibroelastosis
• Histologically confirmed pleuroparenchymal fibroelastosis on the recipient lungs

Exclusion criteria

• All other interstitial lung disease than pleuroparenchymal fibroelastosis
• Pleuroparenchymal fibroelastosis who didn't underwent lung transplantation

Trial design

30 participants in 1 patient group

lung transplantation

Description:

Lung transplantation performed for end-stage interstitial lung disease secondary to pleuroparenchymal fibroelastosis.

Treatment:

Procedure: Lung transplantation (single, lobar or bilateral lung transplantation)